What is hemophagocytic syndrome, and can it be cured when caused by EB virus infection?
Feb 22, 2023
Source: Cainiu Health
Dr. Jiang Weimin
Introduction
Hemophagocytic syndrome is an immune system disorder caused by Epstein-Barr virus (EBV) infection, and most cases can be cured. EBV infection is a rare genetic disease, also known as hemophagocytic syndrome. It is caused by a genetic mutation that leads to fragility of the skin and other soft tissues such as mucous membranes, making them prone to rupture and bleeding.
Hemophagocytic syndrome is an immune system disorder caused by Epstein-Barr virus (EBV) infection, and most cases can be cured.
EB virus infection is a rare genetic disorder, also known as hemophagocytic syndrome. It is caused by a genetic mutation that leads to fragile skin and other soft tissues such as mucous membranes, making them prone to rupture and bleeding. Viral infection further weakens the skin, causing bruising, itching, burning sensations, and pain. Additionally, it may cause damage to other organs, including the gastrointestinal tract, liver, kidneys, and heart. Treatment generally includes supportive care, medication, and surgical intervention.
Most patients can achieve a cure if they receive timely, targeted treatment and have relatively good physical health.
Supportive care is primarily suitable for children or elderly individuals with extremely weak constitutions. Discomfort can be alleviated through systematic treatment and enhanced post-treatment care, such as avoiding exposure to extreme temperatures, maintaining skin cleanliness, refraining from rubbing the skin, and wearing soft clothing.
Medication treatment may include drugs such as ibuprofen tablets, acyclovir tablets, and ganciclovir tablets, used under a doctor's guidance.
Surgical treatment is generally reserved for severe cases where medical therapy has shown no significant effect. In such situations, hematopoietic stem cell transplantation should be performed promptly under medical supervision.
